What RAMSAY HUNT SYNDROME I means: Ramsay Hunt Syndrome I - is a rare and nebulous entity that has alternatively been called dyssynergia cerebellaris myoclonica, dyssynergia cerebellaris progressiva, dentatorubral degeneration, or Ramsay Hunt cerebellar syndrome. Characterized by seizures, cognitive impairment, action myoclonus, and progressive ataxia. Symptoms include seizures, tremor, and reduced muscle coordination. Myoclonus and seizures may be treated with drugs like valproate. RHS type 1 is caused by the impairment of a regulatory mechanism between cerebellar and brainstem nuclei and has been associated with a wide range of diseases, including Lafora disease and celiac disease.
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- Dictionary Infantile - (IRD) is one of a small group of genetic diseases called peroxisome biogenesis disorders (PBD), which are part of a larger group of diseases called the leukodystrophies. These are ramsay hunt syndrome i definition.
- Definition Riley-Day Syndrome:
- Dictionary A very rare congenital disorder of the autonomic nervous system, occurring almost exclusively in Ashkenazi Jewish children. Symptoms include lack of tears, emotional instability, relative ramsay hunt syndrome i explain.
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- Dictionary Adult Refsum disease (ARD) is one of a group of genetic diseases called leukodystrophies, which damage the white matter of the brain and affect motor movements. Due to a genetic abnormality, people ramsay hunt syndrome i what is.
- Definition Rheumatic Encephalitis - Sydenham Chorea (SD):
- Dictionary Encephalitis - Sydenham chorea (SD) is a neurological disorder of childhood resulting from infection via Group A beta-hemolytic streptococcus (GABHS), the bacterium that causes rheumatic fever. SD is ramsay hunt syndrome i meaning.
